Amyotrophic Lateral Sclerosis
NEJM 377:162-172, Brown, R.H.,et al, 2017
Wolfram Syndrome:Hereditary Diabetes Mellitus with Brainstem and Optic Atrophy
Ann Neurol 39:352-360, Scolding,N.J.,et al, 1996
Neurodegeneration and Diabetes:UK Nationwide Study of Wolfram (DIDMOAD) Syndrome
Lancet 1458-1463, Barrett,T.G.,et al, 1995
Spinal Muscular Atrophy
UpToDate, Oct, Bodamer,O.A., 2022
A 42-year-old man with unilateral leg weakness
Neurol 90:e1085-e1090, Schneider, R.,et al, 2018
Mechanisms, Causes, and Effects of Hypercapnia
UptoDate Dec, Feller-Kopman, D.J. & Schwartzstein, R.M., 2016
The Acquired Metabolic Disorders of the Nervous System, Ischemic-Hypoxic Encephalopathy
Adams & Victors Principles of Neurology Chp 40, pg 1133, Ropper, A.H.,et al, 2014
Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Acute Anterior Poliomyelitis
Adams & Victors Principles of Neurology, Chp 33, pg 763, Ropper, A.H.,et al, 2014
Degenerative Diseases of the Nervous System, Progressive Bulbar Palsy
Adams & Victors Principles of Neurology, Chp 39, pg 1111, Ropper, A.H.,et al, 2014
Practice Parameter Update: The Care of the Patient with Amyotrophic Lateral Sclerosis: Drug, Nutritional, and Respiratory Therapies (An Evidence-Based Review)
Neurol 73:1218-1226, Miller,R.G.,et al, 2009
Diagnosis and Management of Motor Neurone Disease
BMJ 336:658-662, McDermott,C.J. &Shaw,P.J., 2008
Glycogen-Storage Disease Type II
eMedicine, May 2, Ibrahim,J. &McGovern,M., 2006
Clinicopath Conf,Encephalomyelitis Due to West Nile Virus and CLL, Case 22-2005
NEJM 353:287-295, Hollande,H.,et al, 2005
ALS Patients on TPPV
Neurol 61:135-137, Hayashi,H. &Oppenheimer,E.A., 2003
A Poliomyelitis-like Syndrome from West Nile Virus Infection
NEJM 347:1279-1280, Leis,A.A., et al, 2002
Nonpoliovirus Poliomyelitis Simulating Guillain-Barre Syndrome
Arch Neurol 58:1460-1464, Gorson,K.C.&Ropper,A.H., 2001
Practice Parameter:The Care of the Patient with Amyotrophic Lateral Sclerosis (An Evidence-Based Review), Report of the Quality Standards Subcommittee of the AAN
Neurol 52:1311-1323, Miller,R.G.,et al, 1999
Poliomyelitis-Like Illness Due to Japanese Encephalitis Virus
lancet 351:1094-1097, Solomon,T.,et al, 1998
Effect of Noninvasive Positive-Pressure Ventilation on Survival in Amyotrophic Lateral Sclerosis
Ann Int Med 127:450-453, Aboussouan,L.S.,et al, 1997
Is Chronic Respiratory Failure in Neuromuscular Diseases Worth Treating
JNNP 61:1-3, Shneerson,J.M., 1996
Motor Neuron Disease
BMJ 313:244, Shneerson,J.M., 1996
Motor Neuron Disease Presenting as Acute Respiratory Failure:A Clinical and Pathological Study
JNNP 60:455-458, Chen,R.,et al, 1996
Three Get Ready
Arch Neurol 53:1222-1223, Goldblatt,D., 1996
Needle Electromyography in the Thoracic Paraspinal Muscles of Motor Neuron Disease
No to Shinkei-Brain & Nerve 48:637-642996., Kyuno,K.,et al, 1996
Motor Neuron Disease
JNNP 57:886-896, Leigh,P.N.&Ray-Chaudhuri,K., 1994
Home Ventilation for ALS Patients:Outcomes, Costs, and Patient, Family and Physician Attitudes
Neurol 43:438-443, Moss,A.H.,et al, 1993
Motor Neurone Disease
BMJ 304:459-460, Norris,F.H., 1992
Motor Neurone Disease:A Hospice Perspective
BMJ 304:471-473, O'Brien,T.,et al, 1992
Anti-Hu-Associated Pareneoplastic Encephalomyelitis/Sensory Neuronopathy
Medicine 71:59-72, Dalmau,J.,et al, 1992
Acute Respiratory Failure from Dopamine Agonist Withdrawal
Neurol 42:1843-1844, Riley,D.E.,et al, 1992
Clinicopath Conf
Motor Neuron Disease, Progressive-Muscular-Atrophy Type, Case 43-1992, NEJM 327:1298-130592., , 1992
Respiratory Complications and Their Management in Motor Neuron Disease
Brain 112:1155-1170, Howard,R.S.,et al, 1989
Diaphragm Pacing for Ventilatory Insufficiency
J Inten Care Med 2:345-353, Marcy,T.W.&Loke,J.S., 1987
Amyotrophic Lateral Sclerosis:Part 1. Clinical Features, Pathology, & Ethical Issues in Management
Ann Neurol 18:271-280, Tandan,R.,et al, 1985
Acute Respiratory Failure in Motor Neuron Disease
Arch Neurol 40:30-32, Hill,R.,et al, 1983
Long-Term Management of Respiratory Failure in Amyotrophic Lateral Sclerosis
Ann Neurol 12:18-23, Sivak,E.,et al, 1982
Management of Hypoventilation in Motor Neuron Disease Presenting with Respiratory Insufficiency
Ann Neurol 7:188-191, Sivak,E.D.,et al, 1980
Spirometry in Amyotrophic Lateral Sclerosis
Arch Neurol 36:74-80, Fallat,R.J.,et al, 1979
Diaphragmatic Paralysis in Motor Neuron Disease
Neurol 28:18, Parhad,I.M.,et al, 1978